Ectopic cordis is a rare congenital anomaly. Here, the fetal heart is displaced outside the thoracic cavity partially or completely. We describe a case of antenatal diagnosis of Thoracic Ectopia Cordis (EC) with congenital heart disease (CHD) without any other extracardiac malformations. Fetal Echocardiographic examination showed large VSD, double outlet right ventricle and unrestricted pulmonary and systemic blood flow. The diagnosis of Ectopia cordis and associated cardiac and non-cardiac anomalies may be difficult in the fetal period due to multiple factors, so meticulous attention should be paid for proper diagnosis.